Selected Lab Publications
- Full Text Available
Current Publications 2009-2013
Bhatara, A., Quintin, E.M., Levy, B., Bellugi, U., Fombonne, E., & Levitin, D.J. (2010). Perception of emotion in musical performance in adolescents with Autism spectrum disorder. Autism Research, 3, 214-225. (PMCID: PMC2963682) PubMed
Bellugi, U., Klima, E.S., & Hickok (2010). Brain organization: Clues from deaf signers with left or right hemisphere lesions. In L. Clara (Ed)., Gesture and Word. Lisbon, Portugal.
Cohen, J.D., Mock, J.R., Nichols, T., Zadina, J., Corey, D.M., Lemen, L., Bellugi, U., Galburada, Reiss, A., & Foundas, A.L. (2010). Morphometry of human insular cortex and insular reduction in Williams syndrome. Journal of Psychiatric Research, 44, 81-89. (PMCID: PMC2813413) PubMed
Collette, J. C., Chen, X.-N., Mills, D.L., Galaburda, A.M., Reiss, A.L., Bellugi, U., & Korenberg, J.R. (2009). Williams Syndrome: Gene expression is related to parental origin and regional coordinate control. Journal of Human Genetics, 54(4), 193-8.
(NIHMSID: NIHMS146394) PubMed
Corina, D., Grosvald, M., & Lachaud, C. (2010, accepted). Perceptual invariance or orientation specificity in American Sign Language? Evidence from repetition priming for signs and gestures. Language and Cognitive Process.
Dai, L., Carter, C.S., Ying, J., Bellugi, U., Pournajafi-Nazarloo,H., & Korenberg, J. (2012). Oxytocin and vasopressin are dysregulated in Williams syndrome, a genetic disorder affecting social behavior. PLoS One, 7(6): e38513. (PMCID: PMC3373592)
Dai, L., Bellugi U., Chen X.N., Pulst-Korenbeg A.M., Järvinen-Pasley A., Tirosh-Wagner T., Eis P.S., Graham, J., Mills D., Searcy Y., & Korenberg J.R. (2009). Is it Williams syndrome? GTF2IRD1 implicated in visual-spatial construction and GTF2I in sociability revealed by high resolution arrays. American Journal of Medical Genetics, 149A(3), 302-314. (PMCID: PMC2650741) PubMed
Emmorey, K., Xum J., Gannon, P., Goldin-Meadow, S., & Braun, A. (2010). CNS activation and regional connectivity during pantomime observation: No engagment of the mirror neuron system for dealf singers. Neuroimage, 49(1), 994-1005. (PMCID: PMC2769569) PubMed
Fishman, I., Ng, R., & Bellugi, U. (2012). Neural processing of race by individuals with Williams syndrome: Do they show the other-race effect? (And why it matters). Social Neuroscience, 7(4): 373-84. PMCID: PMC3401182 PubMed
Fishman, I., Ng, R., & Bellugi, U. (2011). Neural processing of race by individuals with Williams Syndrome: Do they show the other-race effect? (And why it matters). Social Neuroscience. [Epub Ahead of Print] PubMed
Fishman, I., Yam, A., Bellugi, U., & Mills, D. (2011). Language and sociability: Insights from Williams syndrome. Journal of Neurodevelopmental Disorders, 3(3), 185-192. (PMCID:PMC3261273) PubMed
Fishman, I., Yam, A., Bellugi, U., Lincoln, A., & Mills, D. (2010). Contrasting patterns of language associated brain activity in Autism and Williams syndrome. Scan Cognitive and Affective Neuroscience, 6(5), 630-8. (PMCID:PMC3190203) PubMed
Fishman, I., Ng, R., & Bellugi, R. (2010, in press). Do extraverts process social stimuli differently from introverts. Cognitive Neuroscience, 2(2), 67-73. (PMCID: PMC3129862) PubMed
Gao, M.C., Bellugi, U., Dai, L., Mills, D.L., Sobel, E.M., Lange, K., & Korenberg, J.R. (2010). Intelligence in Williams syndrome is related to STX1A, which encodes a component of the presynaptic SNARE Complex. PLoS, 5(4), e10292 (PMCID: PMC2858212) PubMed
Golarai, G., Hong, S., Haas, B., Galaburda, A.M., Mills, D., Bellugi, U., Grill-Spector, K., & Reiss, A.L. (2010). The fusiform face area is enlarged in Williams syndrome. The Journal of Neuroscience, 30(19), 6700-12. (NIHMSID: NIHMS204166) PubMed
Gupta, R. (2011). Attentional, visual, and emotional mechanism of face processing proficiency in Williams syndrome. Frontier in Behavioral Neuroscience, 5(8), 1-2. PMCID: PM307442 PubMed
Haas, BW. & Reiss, A.L. (2012). Social brain development in Williams syndrome: The current status and directions for future research. Frontiers in Psycohology, 3: 186. PMCID: PMC3370330 PubMed
Haas, B.W., Hoeft, F., Barnea-Goraly, N., Golarai, G., Bellugi, U, & Reiss, A. (2012). Preliminary evidence of abnormal white matter related to the fusiform gyrus in Williams syndrome: A diffusion tensor imaging tractography study. Genes Brain Behavior, 11: 62-68. PubMed
Haas, B.W., Hoeft, F., Searcy, Y.M., Mills, D., Bellugi, U., & Reiss, A. (2010). Individual differences in social behavior predict amygdala response to fearful facial expressions in Williams syndrome. Neuropsychologia, 48(5), 1283-8. (NIHMSID: NIHMS167449) PubMed
Haas, B.W., Mills, D., Yam, A., Hoeft, F., Bellugi, U., & Reiss, A. (2009). Genetic influences on sociability: Heightened amygdala reactivity and event-related responses to positive social stimuli in Williams syndrome. The Journal of Neuroscience, 29(4), 1132-9. (PMID: 19176822) PubMed Press Release
Hickok, G. (2010). The role of mirror neurons in speech perception and action word semantics. Psychology Press, [Epub ahead of print].
Hickok, G. (2010). The role of mirror neurons in speech and language processing. Brain and Language, 112(1), 1-2. (PMCID: PMC2813993) PubMed
Hickok, G., & Bellugi, U. (2010). Neural organization of language: Clues from sign language aphasia. In J. Guendouzi, F. Loncke, & M. Williams (Eds.). The Handbook of Psycholinguistic & Cognitive Processes: Perspectives in Communication Disorders. Taylor & Francis (pp. 685-706).
Hickok, G., Pickell, H., Klima, E.S., & Bellugi, U. (2009). Neural Dissociation in the Production of Lexical versus Classifier Signs in ASL: Distinct Patterns of Hemispheric Asymmetry. Neuropsychologia, 47(2), 382-7. (PMCID: PMC2667203) PubMed
Issac, L., & Lincoln. (2011). Featural versus configural face processing in a rare genetic disorder: Williams syndrome. Journal of Intellectual Disability Research. PubMed
Järvinen, A., Dering, B., Neumann, D., Ng, R., Crivelli, D., Grichanik, M., Lai, P., Arnold, A., Korenberg, J.R., and Bellugi, U. (2012). Sensitivity of the autonomic nervous system to visual and auditory affect across social and non-social domains in Williams syndrome. Frontiers in Psychology, Defining Social Phenotypes in Neurodevelopmental Disorders. PMCID: PMC3442284 Pubmed
Jarvinen, A, Korenberg, J.R., & Bellugi, U. (2013). The Social Phenotype of Williams Syndrome. Current Opinions in Neurobiology. (PMID: 23332975) Pubmed
Järvinen-Pasley, A., Adolphs, R., Yam, A., Hill, K.J., Grichanik, M., Reilly, J., Mills, D., Reiss, A.L., Korenberg, J.R., & Bellugi, U. (2010). Affiliative behavior in Williams syndrome: Social perception and real-life social behavior. Neuropsychologica, 48(7), 2110-9 (PMCID: PMC2881624) PubMed
Järvinen-Pasley, A., Pollak, S.D., Yam, A., Hill, K.J., Grichanik, M., Mills, D., Reiss, A., Korenberg, J.R., & Bellugi, U. (2010). Atypical hemispheric assymetry in the perception of negative human vocalizations in individuals with Williams syndrome. Neuropsychologia, 48(4), 1047-1052. (PMCID: PMC2847456) PubMed
Järvinen-Pasley, A., Vines, B. W., Hill, K. J., Yam, A., Grichanik, M., Mills, D., Reiss, A. L., Korenberg, J. R., Bellugi, U. (2010). Cross-modal influences of affect across social and non-Social domains in individuals with Williams syndrome. Neuropsychologia, 48, 456-466. (NIHMS: NIH156758) PubMed
Paul, B., Snyder, A.Z., Haist, F., Raichle, M.E., Bellugi, U., & Stiles, J. (2009). Amygdala response to faces parallels social behavior in Williams syndrome. Social Cognitive and Affective Neuroscience, 4(3), 278-85. (PMCID: PMC2728637)
PubMed
Reilly, J., Lai, P., Bernicot, J., Bellugi, U. (2009). Williams Syndrome: "If you have to have a syndrome, William Syndrome is a cool one to have." In Nass, R. & Y. Frank (Eds). Cognitive and Behavioral Manifestations of Pediatric Diseases. Oxford University Press (pp.267-284).
Stiles, Reilly, Levine, Trauner, Nass (2012). Neural Plasticity and Cognitive Development: Insights from Children with Perinatal Brain Injury. Chapter 8: Later Language Development: Syntax and Discourse. Oxford University Press.
Zitzer-Comfort, C., Reilly, J., Korenberg, J.R., Bellugi, U. (2010). We are social - Therefore we are: The interplay of mind, culture and genetics in Williams syndrome. Formative expeiences: The interactions of caregiving, culture, and developmental psychobiology. Cambridge University Press (pp.133-163).
Published Articles and Chapters: 2000-2008
Atkinson, J., Braddick, O., Rose, F. E., Searcy, Y. M., Wattam-Bell, J., & Bellugi, U. (2006). Dorsal-stream motion processing deficits persist into adulthood in Williams Syndrome. Neuropsychologia, 44(5), 828-833. (PMID: 16168445)
Bellugi, U., Järvinen-Pasley, A., Doyle, T., Reilly, J., & Korenberg, J. (2007). Affect, social behavior and brain in Williams Syndrome. Invited Paper Submitted to Current Directions in Psychological Science, 16(2), 99-104.
Bellugi, U., Klima, E. S., & Korenberg, J. R. (2005). Linking behavior, brain and genes in two different genetic syndromes. In D. Riva, U. Bellugi & M. B. Denckla (Eds.), Neurodevelopmental disorders: Cognitive behavioral phenotypes (pp. 39-58). France: John Libbey Eurotext.
Bellugi, U., & Wang, P.P. (2004). From cognition to brain to gene [CD-ROM]. In G. Adelman and B.H. Smith (Eds.). Encyclopedia of Neuroscience-3rd Edition. Elsevier: Amsterdam, The Netherlands.
Bellugi, U., Lai, Z., & Korenberg, J. (2003). Malattie genetiche, cervello e comportamento. In S. Petruccioli (Ed.), Storia della scienza: Vol 9. (pp. 635-643). Roma: Istituto della Enciclopedia Italiana.
Bellugi, U., Lai, Z.C., & Korenberg, J. (2002). Genes, Brains and Behavior: What Genetic Disorders Reveal about Behavior, pp. 143-153. In D. Baltimore, R. Dulbecco, F. Jacob, & R. Levi-Montalcini (Eds.), Frontiers of Life, San Diego, CA: Academic Press.
Bellugi, U. (2001). Sign Language. In: N. Smelser & P. Baltes (Eds.) International Encyclopedia of the Social and Behavioral Sciences , Vol. 21, pp. 14066-71. Oxford, United Kingdom: Elsevier Science Publishers.
Bellugi U., Korenberg, J.R., & Klima, E.S. (2001) Williams Syndrome: An exploration ofneurocognitive and genetic features. In M. Posner (Ed.) Journal of Clinical Neurosciences Research, Special Issue 1: 217-229.
Bellugi, U., Litchenberger, L., Jones, W., Lai, Z., & St. George, M., (2001). The neurocognitive characterization of Williams Syndrome: A complex pattern of strengths and weaknesses. In U. Bellugi & M. St. George (Eds.), Journey from cognition to brain to gene: Perspectives from Williams syndrome (pp. 1-42). Cambridge, MA: MIT Press. (PMID: 10953231)
Brookes, D.D. (2002). Early lexical development in young children with Williams Syndrome. Unpublished master’s thesis, San Diego State University, San Diego.
Buchsbaum, B., Pickell, B., Love, T., Hatrak, M., Bellugi, U., & Hickok, G. (2005). Neural substrates for verbal working memory in deaf signers: FMRI study and lesion case report. Brain and Language, 95(2), 265-272. (PMID: 16246734)
Chiang, M. C., Reiss, A. L., Lee, A. D., Bellugi, U., Galaburda, A. M., Korenberg, J. R., Mills, D.L., Toga, A. W., & Thompson, P. M. (2007). 3-D pattern of brain abnormalities in Williams syndrome visualized using tensor-based morphometry. Neuroimage, 36(4), 1096-1109. (PMID: 17512756)
Doyle, T.F., Bellugi, U., Korenberg, J.R., & Graham, J. (2004). “Everybody in the world is my friend”: Hypersociability in young children with Williams Syndrome. American Journal of Medical Genetics, 124A, 263-273. (PMID: 14708099)
Eckert, M. A., Galaburda, A., Karchemskiy, A., Liang, A., Thompson, P., Dutton, R. A., Lee, A. D., Bellugi, U., Korenberg, J., Mills, D., Rose, F. E., & Reiss, A. L. (2006). Anomalous sylvian fissure morphology in Williams Syndrome. NeuroImage, 33(1), 39-45. (PMID: 16876437)
Eckert, M., Galaburda, A.M., Mills, D.L., Bellugi, U., Korenberg, J.R., & Reiss, A. (2006). The neurobiology of Williams syndrome: Cascading influences of visual system impairment? Cellular & Molecular Life Sciences, 63(16), 1867-1875. (PMID: 16810457)
Eckert, M., Tenforde, A., Galaburda, A., Bellugi, U., Korenberg, J., Mills, D., & Reiss, A. (2006). To modulate or not to modulate: Differing results in uniquely shaped Williams Syndrome brains. . (PMID: 16806978)
Eckert, M. A., Hu, D., Eliez, S., Bellugi, U., Galaburda, A., Korenberg, J., Mills, D., & Reiss, A. L. (2005). Evidence for superior parietal impairment in Williams Syndrome. Neurology, 64 (1), 152-153. (PMID: 15642924)
Emmorey, K. (2004). Language and Space. In F. Penz, G. Radick, & R. Howell (Eds.). Space (pp. 22-45). Cambridge University Press.
Emmorey, K. & Falgier, B. (2004). Conceptual locations and pronominal reference in American Sign Language. Journal of Psycholinguistic Research, 33(4), 321-331. (PMID: 15360124)
Emmorey, K., Grabowski, T., McCullough, S., Ponto, L, Hichwa, R., & Damasio, H. (2005). The neural correlates of spatial language in English and American sign Language: A PET study with hearing bilinguals, NeuroImage, 24(3), 832-840. (PMID: 15652318)
Emmorey, K. (2003). The neural systems underlying sign language. In M. Marschark & P. Spencer (Eds.). The Handbook of Deaf Studuies, Language, and Education, pp. 361-375. Oxford University Press.
Emmorey, K., & Herzig, M. (2003). Categorical versus gradient properties of classifier constructions in ASL. In K. Emmorey (Ed). Perspectives on classifier constructions in signed languages, pp. 222-246. Mahwah, NJ: Lawrence Erlbaum Associates, Inc.
Emmorey, K., Allen, J.S., Burss, J., Schenker, N., & Damasio, H. (2003). A morphometic analysis of auditory brain regions in congenitally deaf adults. Proceedings National Academy of Science, 100(17), 10049-54. (PMID: 12904582)
Emmorey, K., Grabowski, T., McCullough, S., Damasio, H., Ponto, L., Hichwa, R., & Bellugi, U. (2004). Motor-iconicity of Sign Language does not alter the neural systems underling tool and action naming. Brain and Language, 89(1), 27-37. (PMID: 15010234)
Emmorey, K., McCullough, S., & Brentari, D. (2003). Categorical perception in American Sign Language. Language and Cognitive Processes, 18(1), 21-45.
Emmorey, K. (2002). Mental imagery and embodied cognition: Insights from sign language research. Journal of Mental Imagery, 26, 50-53.
Emmorey, K. (2002). Sign Language and the Brain. Language, cognition, and the brain: Insightsfrom sign language research (pp.271-314). Mahwah, NJ: Lawrence Erlbaum and Associates.
Emmorey, K. (2002). The effects of modality on spatial language: How signers and speakers talk about space. In R. P. Meier. D. G. Quinto, & K. A. Cormier (Eds.), Modality and structure in signed and spoken languages, Cambridge, England: Cambridge University Press.
Emmorey, K., Damasio, H., McCullough, S., Grabowski, T., Ponto, L.L.B., Hichwa, R.D., & Bellugi, U. (2002). Neural system underlying spatial language in American Sign Language. Neuroimage, 17(2), 812-824. (PMID: 12377156)
Emmorey, K. (2001). Space on hand: The exploitation of signing space to illustrate abstract thought. In M. Gattis (Ed.), Spatial schemas and abstract thought, pp. 147-174. Cambridge, MA: The MIT Press.
Emmorey, K. & Casey, S. (2001). Gesture, thought, and spatial language. Gesture 1(1), 35-50.Emmorey, K., Tversky, B., & Taylor, H. (2001). Using space to describe space: Perspective in speech, sign, and gesture. Spatial cognition and computation, 3, 1-24.
Fok, A., Yuen, C.Y., Bellugi, U. & Klima, E. (2001). Visual and Silent Mode of Communication -- The Sign Language used in Hong Kong. A Collection of Papers from the 2001 Conference on the Teaching and Use of Sign Languages edited by the Special Education Section, National Institute of Education, Taiwan pp 8-21.
Galaburda, A.M. & J.E. Schmitt (2003). Neuroanatomic considerations specific to the study of neurogenetics. In G.S. Fisch (Ed.) Genetics and Genomics of Neurobehavioral Disorders. Totowana, NJ: Humana Press, Inc.
Galaburda, A.M., Holinger, D., Mills, D., Reiss, A., Korenberg, J.R., & Bellugi, U. El sindrome de Williams. (2003). [Williams syndrome. A summary of cognitive, electrophysiological, anatomofunctional, microanatomical and genetic findings]. Revista de neurologya [Review of Neurology], 36 (Suppl. 1), S132-S137.
Galaburda, A.M., Holinger, D.P., Bellugi, U., & Sherman, G.F. (2002). Williams syndrome:Neuronal size and neuronal-packing density in primary visual cortex. Archives of Neurology, 59 (9), 1461-1467. (PMID: 12223034)
Galaburda, A. & Bellugi, U (2001). Cellular and moleuclar cortical neuroanatomy in Williams syndrome. In U. Bellugi and M. St. George (Eds.), Journey from cognition to brain to gene: Perspectives from Williams syndrome (pp. 123-146). Cambridge, MA: MIT Press.
Galaburda, A.M., Schmitt, J. E., Atlas, S.W., Eliez, S., Bellugi, U., & Reiss, A.L. (2001). Dorsal forebrain anomaly in Williams syndrome. Archives of Neurology, 58: 1865-1869. (PMID: 11708996)
Gaser, C., Luders, E., Thompson, P. M., Lee, A. D., Dutton, R. A., Geaga, J. A., Hayashi, K. M., Bellugi, U., Galaburda, A. M., Korenberg, J. R., Mills, D. L., Toga, A. W., & Reiss, A. L. (2006). Increased local gyrification mapped in Williams syndrome. NeuroImage, 33(1): 46-54. (PMID: 16901723)
Gothelf, D.,Searcy, Y. M., Reilly, J., Bellugi, U., Lanre-Amos, T., Mills, D., Korenberg, J., Galaburda, A., & Reiss, A. (2008). Association between cerebral shape and social use of language in Williams syndrome. American Journal of Medical Genetics Part A, 146A(21), 2753-2761. (PMID: 18924196)
Gothelf, D., Farber, N., Raveh, E., Apter, A., & Attias, J. (2006). Hyperacusis in Williams syndrome: characteristics and associated neuroaudiologic abnormalities. Neurology, 66(3), 390-395. (PMID: 16476938)
Gothelf, D., Furfaro, J. A., Penniman, L. C., Glover, G. H., & Reiss, A. L. (2005). The contribution of novel brain imaging techniques to understanding the neurobiology of mental retardation and developmental disabilities. Ment Retard Dev Disabil Res Rev, 11(4), 331-339. (PMID: 16240408)
Grossfeld, P.D., Mattina, T., Lai, Z., Favier, R., Lyons Jones, K., Cotter, F., Jones,C., and the 11q Consortium* (2004). The 11q terminal deletion disorder: A prospective study of 110 cases. American Journal of Medical Genetics, 129A(1), 51-61. (PMID: 15266616)
Hickok, G., Pickell, H., Klima, E.S., & Bellugi, U. (2008, in press). Neural Dissociation in the production of lexical versus classier sings in ASL: Distinct patterns of hemispheric assymmetry. Neuropyschologia, [electronic publication ahead of print] (PMID: 18929583)
Hickok, G., Bellugi, U., & Klima, E. S. (2007). Sign language in the brain. In F. E. Bloom (Ed.), Best of the Brain from Scientific American: Mind, Matter, and Tomorrow's Brain. New York: Dana Press, pp. 102-113. (PMID: 11396343)
Hickok, G., & Buchsbaum, B. (2006). Temporal lobe speech perception systems are part of the verbal working memory circuit: evidence from two recent fMRI studies. Behavioral and Brain Sciences.
Hickok, G., Bellugi, U., & Klima E.S. (2002). Sign language in the brain. [Special edition “The Hidden Mind”] Scientific American 12(1), 46-53. (PMID: 11396343)
Hickok, G., Love, T., & Klima, E.S. (2002) Role of the left hemisphere in sign language comprehension. Brain and Language 82, 167-178. (PMID: 12096874)
Hickok, G., & Bellugi, U. (2001). The signs of aphasia [CD-ROM]. In F. Boller & J. Grafman (Series Eds.) & R.S. Berndt (Vol. Ed.), Handbook of neuropsychology: Vol. 3. Language and Aphasia (2nd ed pp 31-50). Amsterdam, The Netherlands: Elsevier Science Publishers; New York: Elsevier Science.
Hickok, G., Bellugi, U., & Klima, E.S. (2001). Sign language in the brain. Scientific American 284 (6), 58-65. (PMID: 11396343)
Hirota, H., Matsuoka, R., Chen, X.N., Salandanan, L.S., Lincoln, A., Rose, F.E., Sunahara, M., Osawa, M., Bellugi, U., & Korenberg, J.R. (2003). Williams syndrome deficits in visual spatial processing linked to GTF2IRD1 and GTF2I on Chromosome 7q11.23. Genetics in Medicine, 5 (4), 311-321. (PMID: 12865760)
Hoeft, F., Barnea-Goraly, N., Haas B.W., Golarai, G., Ng, D., Mills, D., Korenberg, J.R., Bellugi, U., Galaburda, A., & Reiss A.L. (2007). More is not always better: increased fractional anisotropy of superior longitudinal fasciculus associated with poor visuospatial abilities in Williams Syndrome. The Journal of Neuroscience, 27(44), 11960-5.
Holinger, D. P., Bellugi, U., Mills, D. L., Korenberg, J. R., Reiss, A. L., Sherman, G. F., & Galaburda, A. M. (2005). Relative sparing of primary auditory cortex in Williams Syndrome. Brain Res, 1037(1-2), 35-42. (PMID: 15777750)
Jarvinen-Pasley, A., Bellugi, U., Reilly, J., Mills, D. L., Galaburda, A., Reiss, A. L., & Korenberg, J. R. (2008). Defining the social phenotype if Williams Syndrome: A model of linking gene, the brain, and cognition. Development and Psychopathology, 20(1), 1-35. (PMID: 18211726)
Jones, W., Hesselink, J., Courchesne, E., Duncan, T., Matsuda, K., & Bellugi, U. (2002). Cerebellar abnormalities in infants and toddlers with Williams syndrome. Developmental Medicine and Child Neurology, 44, 688-694. (PMID: 12418794)
Jones-Laakmann, W. (2001). Cerebellar contributions to cognition: Evidence from Williams syndrome. Unpublished doctoral dissertation, University of San Diego and San Diego State University.
Jones, W., Bellugi, B., Lai, Z., Chiles, M., Reilly, J., Lincoln, A., & Adolphs, R. (2001). Hypersociability: The socail and affective phenotype of Williams syndrome. In U. Bellugi & M. St. George (Eds.), Journey from cognition to brain to gene: Perspectives from Williams syndrome (pp. 43-72). Cambridge, MA: MIT Press.
Kassubek, J., Hickok, G., & Erhard, P. (2004). Involvement of classical anterior and posterior language areas in sign language production, as investigated by 4 Tesla functional magnetic resonance imaging. Neuroscience Letters, 364, 168-172. (PMID: 15196669)
Klima, E.S., & Bellugi-Klima, U. (2004). Syntactic regularities in the speech of children. In B. Lust & C. Foley (Eds.), First Language Acquisition: The Essential Readings, pp. 344-366, Oxford: Blackwell Publishing. (Reprinted from: Psycholinguistic papers, pp. 183-208, in J. Lyons & R.J. Wales (Eds.), 1966, Edinburgh: Edinburgh University Press).
Korenberg, J. R., Dai, L., Bellugi, U., Jarvinen-Pasley, A., Mills, D., Galaburda, A., Reiss, A., & Pober, B. R. (2008, in press). Deletion of 7q11.23 Genes and Williams Syndrome. In b. C. J. E. second edition, Robert P. Erickson and Anthony Wynshaw-Boris (Ed.), Invited Chapter for Inborn Errors of Development. New York, NY: Oxford University Press.
Korenberg, J.R., Bellugi, U., Salandanan, L.S., Mills, D.L., & Reiss, A.L. (2003). Williams syndrome : A neurogenetic model of human behavior. In Encyclopedia of the Human Genome, pp. 757-766. London, United Kingdom: The Nature Publishing Group.
Korenberg, J.R., Chen, X-N., Hirota, H., Lai, Z., Bellugi, U., Burian, D., Roe, B., & Matsuoka, R. (2000). Genome structure and cognitive map of Williams syndrome. In U. Bellugi & M. St. George (Eds.), Journey from cognition to brain to gene: Perspectives from Williams syndrome (pp. 147-178). Cambridge, MA: MIT Press. (PMID: 10953236)
Lenhoff, H. M., Perales, O., & Hickok, G. S. (2001). Preservation of a normally transient critical period in a cognitively impaired population: window of opportunity for acquiring absolute pitch in Williams Syndrome. In, C. A . Shaw & J. C. McEachern (Eds.) Toward a Theory of Neuroplasticity. Philadelphia: Taylor and Francis Publishers, Psychology Press.
Lenhoff, H. M., Wang, P. P., Greenberg, F., & Bellugi, U. (2006). Williams syndrome and the brain [Electronic version]. Uncommon Genius, Scientific American, 31: 11-15. (PMID: 9388834)
Levitin, D. J., & Bellugi, U. (2006). Rhythm, timbre and hyperacusis in Williams-Beuren syndrome. In C. Morris, H. Lenhoff & P. Wang (Eds.), Williams-Beuren Syndrome: Research and Clinical Perspectives (pp. 343-358). Baltimore, MD: Johns Hopkins University Press.
Levitin, D. J. (2005). Musical behavior in a neurogenetic developmental disorder: evidence from Williams syndrome. Annals of the New York Academy of Sciences, 1060, 325-334. (PMID: 16597782)
Levitin, D. J., Cole, K., Lincoln, A., & Bellugi, U. (2005). Aversion, awareness, and attraction: investigating claims of hyperacusis in the Williams syndrome phenotype. Journal Child Psychology and Psychiatry, 46 (5), 514-523. (PMID: 15845131)
Levitin, D.J., Cole, K., Chiles, M., Lai, Z., Lincoln, A., & Bellugi, U. (2004). Characterizing the musical phenotype in individuals with Williams Syndrome. Child Neuropsychology. 10(4), 223-47. (PMID: 15621847)
Levitin, D. J., Menon, V., Schmitt, J. E., Eliez, S., White, C. D., Glover, G. H., Kadis, J., Korenberg, J. R., Bellugi, U., & Reiss, A. L. (2003). Neural correlates of auditory perception in Williams syndrome: An fMRI study. NeuroImage, 18, 74-82. (PMID: 12507445)
Lincoln, A.J., Searcy, Y.M., Jones, W., Lord, C. & Bellugi, U. (2007). Social interaction behaviors discriminate young children with Autism and Williams Syndrome. Journal of the American Academy of Child and Adolescent Psychiatry. 46(3) 323-331. (PMID: 17314718)
Lincoln, A., Lai, Z., & Jones, W. (2002). Shifting attention and joint attention dissociation in Williams syndrome: Implications for the Cerebellum and the social deficits in Autism. Neurocase 8, 226-232. (PMID: 12119319)
McCullough, S., Emmorey, K., & Sereno, M. (2005). Neural organization for recognition of grammatical and emotional facial expressions in deaf ASL signers and hearing nonsigners. Cognitive Brain Research, 22(2), 193 - 203. (PMID: 15653293)
Mills, D.L., Alvarez, T.D., St. George, M., Appelbaum, L.G., Bellugi, U., & Neville, H. (2001). Electrophysiological studies of face processing in Williams syndrome. In U. Bellugi & M. St. George (Eds.), Journey from cognition to brain to gene: Perspectives from Williams syndrome. (pp. 73-104). Cambridge, MA: MIT Press. (PMID: 10953233)
Mobbs, D., Eckert, M. A., Menon, V., Mills, D., Korenberg, J. R., Galaburda, A. M., Rose, F. E., Bellugi, U., & Reiss, A. L. (2007). Reduced parietal and visual cortical activation during global processing in Williams syndrome. Developmental Medical Child Neurology, 49(6): 433-438. (PMID: 17518929)
Mobbs, D., Eckert, M., Mills, D., Korenberg, J., Galaburda, A., Bellugi, U., & Reiss, A. L (2007, in press). Frontostriatal Dysfunction during Response Inhibition in Williams Syndrome. Biological Psychiatry, 62(3): 256-261. (PMID: 16996488)
Mobbs, D., Garrett, A., Menon, V., Bellugi, U., Rose, F.E. & Reiss, A.L. (2004). Anomalous brain activation during face and gaze processing in Williams syndrome. Neurology, 62(11), 2070-2076. (PMID: 15184616)
Nichols, S., Jones, W. Roman, M., Wulfeck, B. Delis, D. Reilly, J. & Bellugi, U. (2004). Mechanisms of verbal memory impairment in four neurodevelopmental disorders. In B. Wulfeck & J. Reilly (Eds.) Plasticity and Development: Language In Atypical Children, Special Issue Brain and Language, 88, 180-189. (PMID: 14965540)
Pa, J., Wilson, S. M., Pickell, H., Bellugi, U., Hickok, G. (2008). Neural organization of linguistic short-term memory is sensory modality-dependent: Evidence from signed and spoken language. Journal of Cognitive Neuroscience. (PMID: 18457510)
Paul, B., Stiles, J., Passarotti, A., Bavar, N., & Bellugi, U. (2002). Face and place processing in Williams syndrome: Evidence for a dorsal ventral dissociation. NeuroReport 13 (9), 1115-1119. (PMID: 12151752)
Pickell, H., Klima, E., Love, T., Kritchevsky, M., Bellugi, U. & Hickok, G. (2005). Sign language aphasia following right hemisphere damage in a left-hander: a case of reversed cerebral dominance in a deaf signer? Neurocase, 11(3), 194-203. (PMID: 16006340)
Reilly, J., Lacroix, A., Poirier, J., Bernicot, J., Bellugi, U., Klima, E. (2008). Narratives in French and American children with Williams syndrome. Langage et l'homme. (published July 2008).
Reilly, J., Bernicot, J., Vicari, S., Lacroix, A., & Bellugi, U. (2005). Narratives in Children with Williams Syndrome: A Cross Linguistic Perspective. In D. Ravid & H. B.-Z. Shyldkrot (Eds.), Perspectives on language and language development: essays in honor of Ruth A. Berman (pp. 303-312). Dordrecht, the Netherlands: Kluwer.
Reilly, J., Lacroix, A., Poirier, J., Bernicot, J., Bellugi, U., & Klima, E. (2005). Narratives in French and American Children with Williams Syndrome. Le Langage el L’Homme (pp.111- 125).
Reilly, J., Losh, M., Bellugi, U. & Wulfeck, B. (2004). Frog, Where are you? Narratives in children with specific language impairment, early focal brain injury and Williams Syndrome. In B. Wulfeck & J. Reilly (Eds.) Plasticity and Development: Language In Atypical Children, Special Issue Brain and Language, 88, 229-247. (PMID: 14965544)
Reilly, J.S. & Wulfeck, B. (2004). Issues in plasticity and development: Language in atypical children. In B. Wulfeck & J. Reilly (Eds.) Plasticity and Development: Language In Atypical Children, Special Issue Brain and Language, 88, 163-166. (PMID: 14965538)
Reilly, J., Bernicot, J., Vicari, S., Lacroix, A., & Bellugi, U. (2003). Narratives in children with Williams syndrome: A cross linguistic perspective. In D. Ravid & H.B. Shyldkrot (Eds.), Perspectives on language and language development: Essays in honor of Ruth A. Berman. Dordrecht, the Netherlands: Kluwer Publishers.
Reilly, J., Krieter, J., Bellugi, U., Doyle T.F., & Jones, W. (2003). Le langage, l’espace el l’emotion chez des enfants atteints du syndrome de Williams: Une interaction complexe. In. J. Bernicot & J. Reilly (Eds.) Special Issue: d’Enfance Les developpements atypiques du langage chez l’enfant.
Reiss, A. L., Eckert, M. A., Rose, F. E., Karchemskiy, A., Kesler, S., Chang, M., Reynolds, M. F., Kwon, H., & Galaburda, A. (2004). An experiment of nature: Brain anatomy parallels cognition and behavior in Williams syndrome. The Journal of Neuroscience, 24(21), 5009-5015. (PMID: 15163693)
Reiss, A.L., Eliez, S., Schmitt, J.E., Patwardhan, A.J., & Haberecht, M. (2000). Brain imaging in neurogenetic conditions: Realizing the potential of behavioral neurogenetics research. Mental Retardation and Developmental Disabilities Research Reviews , 6 (3):186-197. (PMID: 10982496)
Reiss, A. L., Eliez, S., Schmitt, E., Straus, E., Lai, Z., Jones, W., & Bellugi, U. (2001). Neuroanatomy of Williams syndrome: A high-resolution MRI study. In U. Bellugi & M. St. George (Eds.), Journey from cognition to brain to gene: Perspectives from Williams syndrome (pp.105-122). Cambridge, MA: MIT Press. (PMID: 10953234)
Rose, F.E., Lincoln, A.J., Lai, Z., Ene, M., Searcy, Y.M., & Bellugi, U. (2007). Orientation and affective expression effects on face recognition in Williams syndrome and autism. Journal of Autism & Developmental Disorders, 37: 513-522. (PMID: 16906460)
Searcy, Y.M., Lincoln, A.J., Rose, F.E., Klima, E.S., Bavar, N. & Korenberg, J.R. (2004). The relationship between age and IQ in adults with Williams syndrome. American Journal on Mental Retardation, 109(3), 231-236. (PMID: 15072519)
Schmitt, J.E., Watts, K., Eliez, S., Bellugi, U., Galaburda, A.M. & Reiss, A., (2002) Increased gyrification in Williams syndrome: evidence using 3D MRI methods. Developmental Medicine and Child Neurology, 44 (5), 292-295. (PMID: 12033713)
Schmitt, J.E., Eliez, S., Bellugi, U., & Reiss, A.L. (2001) Analysis of cerebral shape in Williams syndrome. Archives of Neurology, 58 (2), 283-287. (PMID: 11176967)
Schmitt, J.E., Eliez, S., Warsofsky, I., Bellugi, U., & Reiss. A.L. (2001). Enlarged cerebellar vermis in Williams Syndrome. Journal of Psychiatric Research, 35, 225-229. (PMID: 11578640)
Schmitt, J.E., Eliez, S., Warsofsky, I.S., Bellugi, U. & Reiss, A.L. (2001) Corpus callosum morphology of Williams syndrome: Relation to genetics and behavior. Developmental Medical Child Neurology; 43 (3): 155-159. (PMID: 11263684)
Schul, R. (2002). The development of visuospatial attentional orienting: Evidence from normally developing children, children with Specific Language Impairment, and adults with Williams Syndrome. Unpublished doctoral dissertation, University of San Diego and San Diego State University.
Shi, Y., Reiss, A. L., Lee, A. D., Dutton, R. A., Bellugi, U., Galaburda, A. M., Korenberg, J. R.,Mills, D. L., Dinov, I. D., Thompson, P. M., Toga, A. W. (2008) Hamilton-Jacobi skeletons on cortical surfaces with applications in characterizing the gyrification pattern in Williams syndrome. 660-663. (July 2008 to Institute of Electrical and Electronics Engineers) 
Thompson, P. M., Lee, A. D., Dutton, R. A., Geaga, J. A., Hayashi, K. M., Eckert, M. A., Bellugi, U., Galaburda, A. M., Korenberg, J. R., Mills, D. L., Toga, A. W., & Reiss, A. L. (2005). Abnormal cortical complexity and thickness profiles mapped in Williams syndrome. J Neurosci, 25 (16), 4146-4158. (PMID: 15843618)
Tosun, D., Reiss, A. L., Lee, A. D., Dutton, R. A., Hayashi, K. M., Bellugi, U., Galaburda, A. M., Korenberg, J. R., Mills, D. L., Toga, A. W., Thompson, P. M. Use of 3-D cortical morphometry for mapping increased cortical gyrification and complexity in Williams syndrome. 1172-1175. (July 2008 to Institute of Electrical and Electronics Engineers)
Tosun, D., Reiss, A. L., Lee, A. D., Dutton, R. A., Geaga, J. A., Hayashi, K. M., Eckert, M. A., Bellugi, U., Galaburda, A. M., Korenberg, J. R., Mills, D. L., Toga, A. W., & Thompson, P. (2006, accepted for presentation at 2006 IEEE International Symposium on Biomedical Imaging). Use of 3-D cortical morphometry for mapping increased cortical gyrification and complexity in Williams syndrome.
Van Essen, D., Dieker, D., Snyder, A., Raichle, M., Reiss, A., & Korenberg, J. R. (2006). Symmetry of Cortical Folding Abnormalities in Williams Syndrome Revealed by Surface-Based Analyses. J Neuroscience May 17, 2006, 26(20) 5470-83. (PMID: 16707799)
Weiss, D. (2001) Histometric Underpinnings of cerebellar changes in Williams syndrome. Unpublished doctoral dissertation, University of Harvard, Massachusetts.
Wilson, M., & Emmorey, K. (2003). The effect of irrelevant visual input on working memory for sign language. Journal of Deaf Studies and Deaf Education, 8(2), 97-103. (PMID: 15448060)
Wilson, M. & Emmorey, K. (2001). Functional consequences of modality: Spatial coding in working memory for signs. In V. Dively, M. Metzger, S. Taub, & A. M. Baer (Eds.), Sign Languages: Discoveries from international research, pp. 91-99, Gallaudet University Press: Washington, D.C.
Wijesuriya, H. (2002). The role of imprinted gene expression in Williams syndrome. Unpublished master’s thesis, California State University, Los Angeles.
Yang, T.T., Menon, V., Eliez, S., Blasey, C.M., White, C.D., Gotlib, I.H., Reiss, A.L. (2002). Amygdalar activation associated with positive and negative facial expressions. NeuroReport 13 (14), 1737-1741. (PMID: 12395114)
Zitzer-Comfort, C., Doyle, T., Masataka, N., Korenberg, J., & Bellugi, U. (2007). Nature and nurture: Williams syndrome across cultures. Developmental Science, 10(6): 755-62. (PMID: 17973792)
Zitzer-Comfort, C. (2002). Living in a Hello World: The interplay of language, cognition, genetics and culture in Williams syndrome. Unpublished doctoral dissertation, California Polytechnic University, Pomona.
Published Articles and Chapters: 1990-1999
Anderson, S.W., Damasio, H., Damasio, A.R., Klima E.S., Bellugi, U., & Brandt, J.P. (1992). Sign language acquistion following left hemisphere damage and aphasia. Neuropsychologia, 30(4), 329-340. (PMID: 1376447)
Bellugi, U., Adolphs, R., Cassady, C., & Chiles, M. (1999). Towards the neural basis for hypersociability in a genetic syndrome. Neuroreport, 8, 1653-7. (PMID: 10501552)
Bellugi, U., Lichtenberger, L., Mills, D., Galaburda, A., & Korenberg, J.R. (1999). Bridging cognition, the brain and molecular genetics: evidence from Williams Syndrome. Trends in Neuroscience, 22(5), 197-207. Review. (PMID: 10322491)
Bellugi, U., Hickok, G., & Klima, E.S. (1997). Sign language aphasia: A window on the neural basis of language. Scientific American.
Bellugi, U. & Klima, E.S. (1997). Language, spatial cognition and the brain. In M. Ito, Y. Miyashita & E.T. Rolls (Eds.), Cognition, computation and consciousness, 177-189. Cambridge, England: Oxford University Press.
Bellugi, U. & Hickok, G. (1995). Clues to the neurobiology of language. In R. Broadwell (Ed.), Neuroscience, memory, and language: Decade of the brain, volume 1, 89-107. Washington, DC: Library of Congress.
Bellugi, U., Poizner, H., & Klima, E.S. (1993). Language, modality and the brain. In M.H. Johnson (Ed.), Brain development and cognition, 403-423. Cambridge, MA: Blackwell Publishers. (PMID: 2479135)
Bellugi, U. (1993). Language, spatial cognition, and neuronal plasticity. Proceedings of the American Psychiatric Association.
Bellugi, U. (1992). Language, spatial cognition and brain organization. In The Neuronal Basis of Cognitive Function, 207-222. New York, NY: Thieme Medical Publishers.
Bellugi, U. (1991). The link between hand and brain: Implications from a visual language. In D. Martin (Ed.), Advances in Cognition, Education and Deafness. Washington, DC: Gallaudet University Press, 11-35.
Bellugi, U. (1991). Language and cognition: What the hands reveal about the brain. Abstract, Society for Neuroscience, 17(2), 581.
Bellugi, U., Bihrle, A., Jernigan, T., Trauner, D., & Doherty, S. (1990). Neuropsychological, neurological, and neuroanatomical profile of Williams Syndrome. American Journal of Medical Genetics, 6, 115-25. (PMID: 2144426)
Bellugi, U., O'Grady, L., Lillo-Martin, D., O'Grady, M., van Hoek, K., & Corina, D.P. (1990). Enhancement of spatial cognition in deaf children. In V. Volterra & C.J. Erting (Eds.), From gesture to language in hearing and deaf children, 278-298. New York: Springer-Verlag, 21.
Bellugi, U. & Klima, E.S. (1990). Properties of visual spatial languages. In S. Prillwitz & T. Vollhaber (Eds.), Sign Language Research and Application: Proceedings of the International Congress. Hamburg, Germany: Signum-Verlag Press, 15-25.
Bellugi, U., Poizner, H., & Klima, E.S. (1990). Mapping brain functions for language: Evidence from sign language. In G.M. Edelman, W.E. Gall, & W.M. Cowan (Eds.), Signal and sense: Local and global order in perceptual maps, 521-543. New York: Wiley-Liss.
Bettger, J.G., Emmorey, K., McCullough, S.H., & Bellugi, U. (1997). Enhanced facial discrimination: Effects of experience with American Sign Language. Journal of Deaf Studies and Deaf Education, 2(4), 223-233. (PMID: 15579850)
Clark, K., Hickok, G., Love, T., Klima, E.S., Bellugi, U. (1997). Right hemisphere damage aphasia in American Sign Language. Brain and Language, 60, 179-180.
Corina, D.P., Bellugi, U., & Reilly, K. (1999). Neuropsychological studies of linguistic and affective facial expressions in deaf signers. Language and Speech, 2, 307-31. (PMID: 10767992)
Corina, D.P., Kritchevsky, M., & Bellugi, U. (1996). Visual language processing and unilateral neglect: Evidence from American Sign Language. Cognitive Neuropsychology, 13(3), 321-356.
Corina, D.P., Poizner, H., Bellugi, U., Feinberg, T., Dowd, D., & O'Grady-Batch, L. (1992). Dissociation between linguistics and non linguistics gestural systems: A case for Compositionality. Brain and Language, 43(3), 414-447. (PMID: 1446211)
Corina, D.P., Kritchevsky, M., & Bellugi, U. (1992). Linguistics permeability of unilateral neglect: Evidence from American Sign Language. In Proceedings of the 14th Annual Conference of the Cognitive Science Society. Hillsdale, NJ: Lawrence Erlbaum Associates, 384-389.
Corina, D.P., Valid, J., & Bellugi, U. (1992), The linguistics basis of left hemisphere specialization. Science, 255, 1258-1260. (PMID: 1546327)
Corina, D.P., Kritchevsky, M., & Bellugi, U. (1992). Attentional difference in language and object recognition: Evidence from ASL. Abstract, Academy of Aphasia, 25-26.
Emmorey, K., Klima, E.S., & Hickok, G. (1998). Mental rotation within linguistic and non-linguistic domains in users of American sign language. Cognition, 68, 221-246. (PMID: 9852666)
Emmorey, K. (1998). The impact of sign language use on visuospatial cognition. In M. Marschark & D. Clark (Eds.), Psychological perspectives on deafness, 19-52. Hillsdale, NJ: Lawrence Erlbaum and Associates.
Emmorey, K. (1996). The confluence of space and language in signed languages. In O. Bloom, M. Peterson, L. Nadel, & M. Garrett (Eds.), Language and space, 171-209. Cambridge, MA: MIT Press.
Emmorey, K. (1995). Language, gestures, and space. Hillsdale, NJ: Lawrence Erlbaum Associates.
Emmorey, K., Corina, D., & Bellugi, U. (1995). Differential processing of topographic and syntactic functions of space. In K. Emmorey & J. Reilly (Eds.), Language, gestures, and space, 43-62. Hillsdale, NJ: Lawrence Erlbaum Associates.
Emmorey, K., Hickok, G., & Klima, E.S. (1995). Differences in mental rotation within linguistic and nonlinguistic domains: Evidence from an ASL signer with right hemisphere damage. Brain and Language, 51(1), 176-179.
Emmorey, K., Kosslyn, S.M., & Bellugi, U. (1993). Visual imagery and visual-spatial language: Enhanced imagery abilities in deaf and hearing ASL signers. Cognition, 46(2), 139-81. (PMID: 8432094)
Friederici, A., Wessels, J., Emmorey, K., & Bellugi, U. (1992). Sensitivity to inflectional morphology in aphasia: A real-time processing perspective. Brain and Language, 43(4), 747-763. (PMID: 1483200)
Galaburda, A.M., Wang, P.P., Bellugi, U. & Rossen, M. (1994). Cytoarchitectonic anomalies in a genetically based disorder: Williams Syndrome. Neuroreport, 5(7), 753-7. (PMID: 8018845)
Haglund, M.M., Ojemann, G.A., Lettich, E., Bellugi, U., & Corina, D. (1993). Dissociation of cortical and single unit activity in spoken and signed languages. Brain and Language, 44, 19-27. (PMID: 8467375)
Hickok., G., Wilson, M., Clark, K., Klima, E.S., Kritchevsky, M., & Bellugi, U. (1999). Discourse deficits following right hemisphere damage in deaf signers. Brain and Language, 66(2), 233-48. (PMID: 10190988)
Hickok, G., Kirk, K., & Bellugi, U. (1998). Hemispheric organization of local and global-level visuospatial processes in deaf signers and its relation to sign language aphasia. Brain and Language, 65(2), 276-86. (PMID: 9784271)
Hickok, G., Bellugi, U., & Klima, E.S. (1998). The basis of neural organization for language: Evidence from sign language aphasia. Reviews in the Neurosciences, 8, 205-222. (PMID: 9548233)
Hickok, G., Bellugi, U., & Klima, E.S. (1998). The neural organization of language: Evidence from sign language aphasia. Trends in Cognitive Sciences, 2, 129-136.
Hickok, G., Bellugi, U., & Klima, E.S. (1998). What's right about the neural organization of sign language? A perspective on recent neuroimaging results. Trends in Cognitive Sciences, 2, 465-468.
Hickok, G., Bellugi, U., & Klima, E.S. (1996). The neurobiology of signed language and its implications for the neural organization of language. Nature, 381, 689-702. (PMID: 8649515).
Hickok, G., Say, K.A., Bellugi, U. & Klima, E.S. (1996). The basis of hemispheric asymmetries for language and spatial cognition: Clues from focal brain damage in two deaf native signers. Aphasiology, 10(6), 577-591.
Hickok, G., Avrutin, S. (1996). Comprehension of WH-questions in two Broca's aphasics. Brain and Language, 52, 314-327. (PMID: 8811962)
Hickok, G., Kritchevsky, M., Bellugi, U., & Klima, E.S. (1996). The role of left frontal operculum in sign language aphasia: Clues to the function of Broca's area. Neurocase, 2, 373-380.
Hickok, G., Klima, E.S., Kritchevsky, M., & Bellugi, U. (1995). A case of "sign blindness" following damage in left occipital cortex in a deaf signer. Neuropsychologia, 33, 1596-1606. (PMID: 8745177)
Hickok, G., Bellugi, U., & Jones, W. (1995). Asymmetrical ability. Science, 270(5234), 219-20. (PMID: 7569963)
Hickok, G., & Avrutin, S. (1995). Representation, referentiality, and processing in agrammatic comprehension. Brain and Language, 50, 10-26.
Jernigan, T.L., Bellugi, U., Sowell, E., Doherty, S., & Hesselink, J.R. (1993). Cerebral morphologic distinctions between Williams and Down Syndromes. Archives of Neurology, 50(2), 186-91. (PMID: 8431138)
Jernigan, T.L. & Bellugi, U. (1990). Anomalous brain morphology on magnetic resonance images in Williams Syndrome and Down Syndrome. Archive of Neurology, 47(5), 529-33. (PMID: 2139774)
Klima, E.S., Tzeng, O., Fok, A., Bellugi, U., Corina, D., & Bettger, J. (1999). From sign to script: Effects of linguistic experience on perceptual categorization. In O.J.L. Tzeng (Ed.) The Biological Bases of Language, Monograph series, 13, Journal of Chinese Linguistics, 96-129.
Klima, E.S. (1990). The neural substrate for sign language. Theoretical Issues in Sign Language Research, Boston, MA.
Lenhoff, H.M., Wang P.P., Greenberg, F., & Bellugi, U. (1997). Williams syndrome and the brain. Scientific American, 277(6), 68-73. (PMID: 9388834)
Mattson, S.N., Riley, E.P., Jernigan, T.L., Ehlers, C.L., Delis, D.C., Jones, K.L., Stern, C., Johnson, K.A., Hesselink, J.R., & Bellugi, U. (1992). Fetal Alcohol Syndrome: A case report of neuropsychological, MRI and EEF assessment of two children. Alcoholism, Clinical and Experimental Research, 16(5), 1001-3. (PMID: 1443415)
Neville, H.J., Coffey, S.A., Lawson, D.S., Fischer, A., Emmorey, K., & Bellugi, U. (1997). Neural systems mediating American Sign Language: Effects of sensory experience and age of acquisition. Brain and Language, (57)3, 285-308. (PMID: 9126418)
Poizner, H., Bellugi, U., & Klima E.S. (1991). Brain function for language: Prespectives from another modality. In I. Mattingly & M. Studdert-Kennedy (Eds.), Modularity and the Motor Theory of Speech Perception. Hillsdale, NJ: Lawrence Erlbaum Associtates, 145-169.
Poizner, H., Bellugi, U., & Klima E.S. (1990). Biological foundations of language: Clues from sign language. Annual Review of Neuroscience, 13, 283-307. (PMID: 2183678)
Reilly, J.S. & Bellugi, U. (1996). Competition on the face: Affect and language in ASL motherese. Journal of Child Language, 23(1), 219-39. (PMID: 8733568)
Reilly, J.S., McIntire, M.L., & Seago, H. (1992). Affective prosody in American Sign Language. Sign Language Studies, 75, 113-128.
Reilly J.S., McIntire, M.L., & Bellugi, U. (1990). The relationship between language and affect. In V. Volterra & C. Erting (Eds.), From Gesture to Language in Hearing and Deaf Children. New York: Srpinger-Verlag, 128-141.
Riche, L., Bellugi, U., Emmorey, K., Bettger, J.G., & Klima, E.S. (1993). The development and breakdown of phonological awareness for ASL. Stanford Child Language Research Forum, Stanford, CA.
van Hoek, K. (1996). Conceptual locations for reference in American Sign Language. In G. Fauconnier & E. Sweetser (Eds.) Spaces, worlds, and grammar, 334-350. Chicago, IL: University of Chicago Press.
van Hoek, K. (1992). Conceptual spaces and pronominal reference in American Sign Language. Nordic Journal of Linguistics, 15(2).
van Hoek, K., O'Grady-Batch, L., & Reilly, J. (1990). The acquisition of spatial language and spatial cognition. Theoretical Issues in Sign Language Research. Boston, MA.
Wang, P.P., Doherty, S., Rourke, S.B., & Bellugi, U. (1995). Unique profile of visuo-perceptual skills in a genetic syndrome. Brain and Cognition, 29(1), 54-65. (PMID: 8845123)
Wang, P.P. & Bellugi, U. (1994). Evidence from two genetic syndromes for a dissociation between verbal and visual-spatial short-term memory. Journal of Clinical and Experimental Neuropsychology, 16(2), 317-22. (PMID: 8021317)
Wang, P.P. & Bellugi, U. (1993). Williams Syndrome, Down Syndrome, and cognitive neuroscience. American Journal of Diseases of Children, 11, 1246-51. (PMID: 8237921)
Wang, P.P., Hesselink, J.R., Jernigan, T.L., Doherty, S., & Bellugi, U. (1992). Specific neurobehavioral profile of Williams' Syndrome is associated with neocerebellar hemispheric preservation. Neurology, 42(10), 1999-2002. (PMID: 1407582)
Wang, P.P., Doherty, S., Hesselink, J.R., & Bellugi, U. (1992). Callosal morphology concurs with neurobehaviroal and neuropathological findings in two neurodevelopmental disorders. Archive of Neurology, 49(4), 407-11. (PMID: 1532713)
Wilson, M., Bettger, J., Niculae, I., & Klima, E.S. (1997). Modality of language shapes working memory: Evidence from digit span and spatial span in ASL signers. Journal of Deaf Studies and Deaf Education, 2(3), 152-162. (PMID: 15579844)
Zein, G., Say, K., Bellugi, U., Corina, D., & Reilly, J. (1993). The role of the right hemisphere extrasyntactic aspects of ASL. Academy of Aphasia, Tucson, AZ.
Revelant Publications:
Allman, J.M., Tetreault, N.A., Hakeem, A.Y., Manaye, K.F., Semendeferi, K., Erwin, J.M., Goubert, V., & Hof, P.R. (2010). The von economo neurons in grontoinsular and anterior cingulate cortex in great apes and humans. Brain Structure and Function, 214, 495-517. PubMed
Brown, T.T., Kuperman, J.M., Erhart, M., White, N.S., Roddey, J.S., Shankarnarayanan, A., Han, E.T., Rettmann, D., & Dale, A.M. (2010). Prospective motion correction of high-resolution magnetic resonance imaging data in children. Neuroimage, 53(1), 139-145. PubMed
Destrieux, C., Fischl, B., Dale, A., & Halgren, E. (2010). Automatic parcellation of human cortical gyri and sulci using standard anatomical nomenclature. Neuroimage, 15, 53(1), 1-15. (PMCID: PMC2937159) PubMed
Fishman, I., Ng, R., & Bellugi, R. (2010, in press). Do extraverts process social stimuli differently from introverts. Cognitive Neuroscience.
Fishman, I., Yam, A., Bellugi, U., & Mills, D. (2010, under review). Language and sociability: Insights from Williams syndrome.
Halgren, E., Sherfey, J., Irimia, A., Dale, A.M., & Marinkovic, K. (2010). Sequential temporo-fronto-temporal activation during monitoring of the auditory environment for temporal patterns. Human Brain Mapping, (Epub ahead of print). PubMed
Korenberg, J.R., Dai, L. Pournajafai-Nazarloo, H., Bellugi, U., & Carter, C.S. (2010). Social neuropeptides oxytocin and vasopressin are dysregulated in Williams syndrome. Program No. 2016/T. American Society for Human Genetics 60th Annual Meeting, Washington, D.C.
Marchetto, M.C.N., Carromeu, C., Acab, A., Yu, D., Yeo, G.W., Mu, Y., Chen, G., Gage, F.H., & Muotri, A.R. (2010). A model for neural development and treat for Rett syndrome using human induced pluripotent stem cells. Cell, 143, 527-539. PubMed
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